探讨肝膈疝合并肺内异位肝的诊疗方案。

回顾性分析1例右侧肝膈疝合并肺内异位肝患者的临床表现、影像学特征、手术治疗方案及病理，对异位肝进行相关的探讨及文献复习。

患者接受胸腔镜肺楔形切除术＋膈疝修补术，术中发现右肺下叶肿物，与疝入胸腔组织不连续。病理结果提示为异位肝组织。患者术后一年复查胸部CT未见异常，随访无特殊不适。

异位肝在临床上极为少见，病例结合相关文献复习，以提高对该病的认识，且腔镜微创手术不仅直观观察，也可直接切除明确诊断且治愈该病。

To explore diagnosis and treatment scheme of diaphragmatic hernia of liver with intrapulmonary ectopic liver.

To review the clinical features, imageology characteristics, surgical management and pathological features of a case of right diaphragmatic hernia of liver with intrapulmonary ectopic liver.

The patient received thoracoscopic pulmonary wedge resection and diaphragmatic hernia repair. A mass in the lower lobe of the right lung was found during the operation, which was not continuous with the herniated tissue into the thoracic cavity. The pathological result showed that the mass was ectopic liver tissues. There was no abnormality in the chest CT scan of the patient one year after the operation, and there was no special discomfort during the follow-up.

The ectopic liver is extremely rare in clinical practice. This case is combined with the review of relevant literature to improve the understanding of the disease. And the thoracoscopic minimally invasive surgery can not only help surgeons to observe intuitively, but also can directly remove the lesions to confirm the diagnosis and cure the disease.